S. Ben Yahia, R. Messaoud, S. Attia, T. Zaafouri, S. Zaouali, A. Ladjimi, M. Khairallah


To report the macular involvement in patients with posterior microphthalmos.


The records of eighteen patients with posterior microphthalmos were reviewed. These included clinical, fundus photographic, fluorescein angiographic, and ultrasonographic findings.


All patients had bilateral foreshortening of the posterior ocular segment (range, 7–11.2 mm) with associated high hyperopia (range, +12.00 to +19.00 diopters) and normal or slightly smaller than normal anterior segment dimensions. Visual acuity ranged from 20/200 to 20/40. Macular involvement included bilateral elevated papillomacular retinal fold (13 patients, 72.2%); fine macular folds (6 patients, 33.3%); macular detachement secondary to uveal effusion syndrome (1 patients, 16.7%); and absence or marked reduction of the capillary-free zone (18 patients, 100%).


Macular changes in patients with posterior microphthalmos mainly include elevated papillomacular retinal fold and absence or marked reduction of the capillary-free zone.

Take-home message:

The macula is usually involved during posterior microphthalmos, explaining in part the visual impairment in these patients.