Authors: Elena Palacios-Pozo, Maria Garcia-Pous, Amparo Navea, M. Carmen Desco, Jorge Mataix, Valencia, Spain

Advantages:

To evaluate the management of retinal detachment and subluxation of the lens in a child with Marfan Syndrome.

Methods:

Marfanʼs syndrome is an autosomic dominant genetic disorder of the elastic fibers of connective tissue. That syndrome affects many body systems (skeletal, ocular, cardiovascular, cutaneous, pulmonary, abdominal, neurological). We report a case of a child 12 years old with Marfanʼs syndrome, with a retinal detachment and subluxation of the lens. Scleral buckling, vitrectomy and pars plana lensectomy were perfomed. Triamcinolone (subtenon) was injected to prevent proliferative vitreoretinopathy.

Effectiveness / Safety:

We recommend the pars plana lensectomy instead of phacoemulsification to decrease the risk of proliferative vitreoretinopathy.