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Albino Fundus 1

              Contact Details: Email: ihabsaad@hotmail.com Cell Phone:...

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Atypical Bilateral Morning Glory Syndrome

Pedro Neves_SCIENTIFIC POSTER 2015 Introduction: Morning Glory Syndrome is a non-hereditary optic nerve malformation, most frequently unilateral and in women, rarely affecting black patients. The optic disk is abnormally excavated and funnel-shaped, with an hypopigmented neuroretinal rim and radially-oriented vessels. Up to one third of patients present with a retinal detachment, and this syndrome may be associated with other craniofacial...

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Re-intervention in De-novo Vitreous Opacities After PPV in Familial Amyloidotic Polyneuropathy in Portuguese Patients

SCIENTIFIC POSTER_Natalia Ferreira Purpose: To report management of de novo vitreous amyloid opacities after previous pars plana vitrectomy in familial amyloidotic polyneuropathy. Methods: Retrospective observational consecutive case series of 4 eyes. Demographic data, TTR mutation involved, age at the beginning of disease, period of evolution of disease, liver transplant, time between total vitrectomy and repeat intervention and the...

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Ocular Manifestations of Familial Amyloidosis Transthyretin V30M Related: Impact of Liver Transplantation

SCIENTIFIC POSTER_Ines Casal_2 Familial amyloidosis TTR V30M is caused by an amino acid substitution of methionine for valine at position 30 of transthyretin (TTR), a transport protein. This leads to an extracellular amyloid deposition in peripheral nerves causing motory, sensory and autonomic neuropathy in solid organs and the eye. The major production of circulating TTR is in the liver, but some production occurs also in the choroid and...

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Familial Amyloidosis TTR V30M: What Happens in the Posterior Segment of the Eye?

SCIENTIFIC POSTER_Ines Casal_1 Familial amyloid polyneuropathy (FAP) is a group of autosomal dominant inherited diseases whose most frequent causative mutation is TTR V30M (a substitution of methionine for valine at position 30 in transthyretin). Transthyretin (TTR) is a normal serum protein which is mainly synthesized in the liver, but also in other tissues such as the choroid plexus and the retinal pigmented epithelium. This disorder is...

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Use of Ranibizumab for Neovascular Glaucoma in a Patient with Familial Amyloidosis Transthyretin V30M Related

SCIENTIFIC POSTER_Ines Casal_3 Introduction: Familial amyloidosis TTR V30M is an autosomal dominant inherited disorder caused by extracellular amyloid deposition in nerves, solid organs and in the eye. Several ocular manifestations were reported such as abnormal conjunctival vessels, keratoconjunctivitis sicca, amyloid deposits at the pupillary margin, glaucoma, deposition of amyloid at the anterior capsula of the lens, vitreous opacities...

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Vitreous Opacities & Retinal Amyloid Microangiopathy in Familial Amyloidotic Polyneuropathy

Familial amyloid polyneuropathy (FAP) is an inherited disorder with autosomal dominant transmission, characterized by systemic extracellular accumulation of amyloid fibrils. The peripheral nervous system and the heart are the main target organs, but the eye may also be involved. The most common type of FAP is related to transthyretin (TTR) and Portugal is an endemic country for FAP TTR Val30Met.TTR is mainly produced by the liver, but a...

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Surgical Management of Persistent Hyperplastic Primary Vitreous

Poster 2 Salim Ben Yahia Advantages: To evaluate the outcome of surgical management of persistent hyperplastic primary vitreous. Methods: Retrospective study including 3 eyes of 3 children with unilateral persistent hyperplastic primary vitreous. Patients were aged 6 years, 4 years, and 2 years respectively. Patients underwent Cataract extraction combined with vitrectomy and removal of embryonic remnants. Intraocular lenses were implanted...

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Modified Vortex Vein Decompression in Idiopathic Ciliochoroidal Effusion

Introduction: Idiopathic ciliochoroidal effusion is a specific pathological entity with abnormal thickened sclera resulting in significant exudative retinal detachment. Methods: 4 cases of idiopathic ciliochoroidal effusion presented with total exudative retinal detachment. Modified vortex vein decompression was performed. Effectiveness / Safety: Flattening of the retina was achieved in all cases. There were no ocular...

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Spontaneous Resolution of Serous Retinal Detachment in a Patient with Congenital Retinal Macrovessel

Francisco J. Ascaso, Esther Nuñez, Laura Lavilla, María A. Del Buey, José A. Cristóbal (Zaragoza, Spain) Advantages: Macular neurosensory retinal detachments (RD) that present in an atypical fashion constitute a diagnostic challenge to retinal specialists. We recommend observation when they are associated with a congenital retinal macrovessel (CRM). Fluorescein angiography (FA) proves to be valuable in establishing a definitive...

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Intravitreal Bevacizumab in Nanophthalmic Exudative Retinal Detachment

Satyen Deka, H Bhattacharjee, H Deka, M J Barman, S M Das (Guwahati, India) Advantages: Currently the only treatment option for exudative RD in nanophthalmic eye is surgical (Scleral Resection) with guarded visual prognosis. Intravitreal bevacizumab is a less invasive and safe treatment used for multiple retinal vascular/inflammatory diseases to treat the macular edema, the mode of action of which is through blockage of VEGF mediated...

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Management of Exudative Retinal Detachment Following Surgery in Nanophthalmic Eyes

Frank Becquet, Jean-François Le Rouic, Didier Ducournau (Nantes, France) Purpose: To report three cases of nanophthalmic uveal effusion syndrome with exudative retinal detachment after intraocular surgery. Methods: Three patients were referred to us with a persistent exudative retinal detachment after intraocular surgery (surgery of glaucoma in two cases and cataract in one case). Sclerectomy and vortex vein decompression were performed...

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Modified Vortex Vein Decompression in Idiopathic Ciliochoroidal Effusion

Ihab Saad Othman (Giza, Egypt) Advantages: Idiopathic ciliochoroidal effusion is a specific pathological entity with abnormal thickened sclera resulting in total exudative retinal detachment. Methods: 4 cases of idiopathic ciliochoroidal effusion presented with total exudative retinal detachment. Modified vortex vein decompression was performed in 2 quadrants by creating a 90% scleral window around the vortex veins and drainage of...

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Exsudative Retinopathy in Incontinentia Pigmenti

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Spontaneous Vitreous Hemorrhage as the First Manifestation of Persistent Hyperplastic Primary Vitreous in an Adult

Evangelia Papavasileiou, D. Dereklis, I. Vasiliadis, F. Topouzis (Thessaloniki, Greece) Advantages: Persistent hyperplastic primary vitreous (PHPV) is a rare developmental malformation of the eye characterized by the presence of a vascular membrane located behind the lens and that is usually unilateral and sporadic. We present a case in which a 25-year old female was referred to our office for reduced visual acuity in the left eye. Visual...

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Surgical Treatment of Exudative Retinal Detachment in Eyes with Nanophthalmus

http://www.evrs.eu/medias/2010/congress/Vascular-Pathologies-in-Young-Patients.flv Sengul Ozdek (Ankara, Turkey) Advantages: Sclerectomy surgery is easy and effective in eyes with exudative RD secondary to nanophthalmos. Methods: Four quadrant deep sclerectomy and sclerostomy with mitomycin C was applied to 6 eyes of 3 patients with exudative RD secondary to nanophthalmos. Effectiveness / Safety: Exudative RD resolved quickly in 4 eyes...

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Diagnosis and Treatment of Incontinentia Pigmenti

http://www.evrs.eu/medias/2010/congress/Vascular-Pathologies-in-Young-Patients.flv Xavier Maseras, Ignasi Jürgens, Montserrat González, Marius Passarell (Barcelona, Spain) Advantages: Incontinentia pigmenti is a rare X-linked dominantly inherited neurocutaneous disorder characterized by unusual patterns of discolored skin. One third of patients with incontinentia pigmenti have ophthalmologic findings including cataract, strabismus, optic...

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